Listar por autor "Amaral, Margarida D."
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Folding Status Is Determinant over Traffic-Competence in Defining CFTR Interactors in the Endoplasmic Reticulum
Santos, João D.; Canato, Sara; Carvalho, Ana S.; Botelho, Hugo M.; Aloria Escolastico, Kerman; Amaral, Margarida D.; Matthiesen, Rune; Falcao, Andre O.; Farinha, Carlos M. (MDPI, 2019-04-14)The most common cystic fibrosis-causing mutation (F508del, present in ~85% of CF patients) leads to CFTR misfolding, which is recognized by the endoplasmic reticulum (ER) quality control (ERQC), resulting in ER retention ...